Hepatic Epithelioid Hemangioendothelioma: A Case Report of an Extremely Rare Tumor

Dr Taleb Khaoula; Dr Lemsyeh Hajar; Dr Abdi Chaimae; Dr Elmabrouk Fatma; Pr Naciri Sara; Pr Elghissassi Ibrahim; Pr Boutayeb Saber; Pr Mrabti Hind; Pr Errihani Hassan

doi:10.36948/ijfmr.2024.v06i04.25080

Hepatic Epithelioid Hemangioendothelioma: A Case Report of an Extremely Rare Tumor

Author(s)	Dr Taleb Khaoula, Dr Lemsyeh Hajar, Dr Abdi Chaimae, Dr Elmabrouk Fatma, Pr Naciri Sara, Pr Elghissassi Ibrahim, Pr Boutayeb Saber, Pr Mrabti Hind, Pr Errihani Hassan
Country	Morocco
Abstract	Epithelioid hemangioendothelioma is a very rare vascular tumour, with fewer than 500 cases described worldwide. Diagnosis is often multifocal or at an advanced stage with non-specific symptoms. Pathological examination by biopsy is crucial to confirm the diagnosis. The liver is the most frequent site of predilection, followed by the lungs and bones. The etiology of hepatic epithelioid hemangioendothelioma is poorly understood and is not linked to chronic liver disease, with a heterogeneous and unpredictable course depending on the individual. Given the rarity of this cancer, there are no established treatment standards for this type of tumor of intermediate malignancy. Surgical resection is performed in the case of unifocal disease, and orthotopic liver transplantation remains an option in the case of multifocal and/or unresectable disease, with high survival rates and disease free survival (DFS). Transcatheter arterial chemoembolization (TACE) and chemotherapy/radiotherapy regimens are other treatment possibilities. However, surveillance may be proposed for asymptomatic patients with a slow progression. We report the case of a patient followed for a multifocal EHE with pulmonary metastases, discovered following pain in the right hypochondrium. Morphological and immunohistochemical examination confirmed the diagnosis of hepatic epithelioid hemangioendothelioma. Given the moderate symptoms, surveillance was recommended for our patient with a good clinical course and radiological stability for 3 years.
Keywords	Epithelioid hemangioendothelioma, Liver, Lung metastasis, Active surveillance, Systemic therapy.
Field	Medical / Pharmacy
Published In	Volume 6, Issue 4, July-August 2024
Published On	2024-07-23
Cite This	Hepatic Epithelioid Hemangioendothelioma: A Case Report of an Extremely Rare Tumor - Dr Taleb Khaoula, Dr Lemsyeh Hajar, Dr Abdi Chaimae, Dr Elmabrouk Fatma, Pr Naciri Sara, Pr Elghissassi Ibrahim, Pr Boutayeb Saber, Pr Mrabti Hind, Pr Errihani Hassan - IJFMR Volume 6, Issue 4, July-August 2024. DOI 10.36948/ijfmr.2024.v06i04.25080
DOI	https://doi.org/10.36948/ijfmr.2024.v06i04.25080
Short DOI	https://doi.org/gt43q8

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Hepatic Epithelioid Hemangioendothelioma: A Case Report of an Extremely Rare Tumor

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